Purity: Free 6HMU < 0.1 %
Biochemical test: Galactocerebrosidase activity in fibroblasts and leukocytes of
classical Krabbe disease < 2 % of mean normal activity.
C32H49NO9 MW: 592
1. A major modification of Wiederschain et al. 1992.
Clin Chim Acta 1992, 205: 87-96.
2. Reliable pre- and postnatal enzyme analysis for Krabbe disease,
using a fluorogenic substrate for galactocerebrosidase.
van Diggelen et al., manuscript in preparation
Order code: KRB
Pack size: 15 mg (maximal 3150 assays)
Price: € 523