6-Hexadecanoylamino-4-methylumbelliferyl-beta-D-galactoside

Purity:                       Free 6HMU < 0.1 %

Biochemical test: Galactocerebrosidase activity in fibroblasts and leukocytes of
classical Krabbe disease < 2 % of mean normal activity.

 

Molecular Formula:

C32H49NO9    MW: 592

Literature reference:

1. A major modification of Wiederschain et al. 1992.
Clin Chim Acta 1992, 205: 87-96.
2. Reliable pre- and postnatal enzyme analysis for Krabbe disease,
using a fluorogenic substrate for galactocerebrosidase.
van Diggelen et al., manuscript in preparation

Order code:  KRB

Pack size:   15 mg    (maximal 3150 assays)

Price:    € 523