4-Methylumbelliferyl a-L-idopyranosiduronic acid 2-sulphate (Moscerdam code: M2)
The substrate without 2nd-step enzymes, is now available from Carbosynth with product code EM 03201
LEBT-M2: NOTE: partially purified enzymes for the 2nd step reaction are NOT available.
Moscerdam and Carbosynth are currently collaborating to make the 2nd step enzyme available by Carbosynth.
A fluorogenic assay for the diagnosis of Hunter disease (MPS II)
Voznyi YV, Keulemans JLM, van Diggelen OP.
J Inher Metab Dis 2001; 24: 675-680.