4-Methylumbelliferyl 2-deoxy-2-Sulfamino-α-D-glucopyranoside
NOTE:
Order from Carbosynth, cat.no. EM06602
Biochemical purity >99.96% (low substrate-blank).
Literature reference:
A fluorogenic assay for the diagnosis of Sanfilippo disease type A
(MPS III A)
Karpova EA, Voznyi YV, Keulemans JLM, Hoogeveen AT,
Winchester B, Tsvetkova I, van Diggelen OP.
J Inher Metab Dis 1996; 19: 278 – 285