4-Methylumbelliferyl-beta-D-glucosaminide

Purity:                    Free 4MU < 0.1 %

 

Biochemical test: Acetyl-CoA : alpha-glucosaminide N-acetyltransferase activity in
fibroblasts and leukocytes of classical Sanfilippo C patients
(MPS III C) < 5.3 % of mean normal activity.

Molecular Formula:

C16H19NO7      MW: 337 

Literature reference: 

A fluorimetric enzyme assay for the diagnosis of Sanfilippo disease C
(MPS IIIC)
Voznyi YV, Karpova EA, Dudukina TV, Tsvetkova IV, Boer AM, 
Janse HC, van Diggelen OP.   J Inh Metab Dis 1993; 16: 465-472