6-Hexadecanoylamino-4-methylumbelliferyl-phosphorylcholine

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Purity:                    Free 6HMU < 0.1 %

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Biochemical test:

Sphingomyelinase activity in fibroblasts and leukocytes from
Niemann-Pick A patients < 4.2 % and < 9 % of mean
normal activity, respectively.

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Molecular Formula:

C31H51N2O7P                 MW: 595

Literature reference: A new fluorimetric enzyme assay for the diagnosis of Niemann-
Pick A/B, with specificity of natural sphingomyelinase substrate.
van Diggelen OP, Voznyi YV, Keulemans JLM, Schoonderwoerd K,
Ledvinova L, Mengel E, Zschiesche M, Santer R, Harzer K.
J Inher Metab Dis 2005; 28: 733-741

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